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Term ID: | 18907 |
Name: | craniopharyngioma |
Definition: | A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. The most significant factor associated with recurrence is the extent of surgical resection, with lesions greater than 5 cm in diameter carrying a markedly worse prognosis. (Adapted from WHO) |
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Synonyms: | Adamantinomatous tumor; craniopharyngeal duct tumor; craniopharyngioma (morphologic abnormality); craniopharyngioma (WHO grade I); craniopharyngioma, benign; cystoma; Dysodontogenic epithelial tumor; neoplasm of Rathke's pouch; Rathke pouch neoplasm; Rathke pouch tumor; Rathke's pouch neoplasm; Rath |
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OMIM: MSeqDR : Genes: | Phenotypes | | Disease Causing ClinVar Variants | | MSeqDR Portal | |
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