Human Disease MESH is developed by UMLS. Further data from MedGen, OMIM, CTD
Term ID:
3240
Name:
Dermatomyositis
Definition:
A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6)
Adult Type Dermatomyositides |Adult Type Dermatomyositis |Childhood Type Dermatomyositides |Childhood Type Dermatomyositis |Dermatomyositides |Dermatomyositides, Adult Type |Dermatomyositides, Childhood Type |Dermatomyositis, Adult Type |Dermatomyositis, Childho
Slim Mappings:
Connective tissue disease|Musculoskeletal disease|Nervous system disease|Skin disease