..Starting node ..Double outlet right ventricle with doubly committed ventricular septal defect and pulmonary stenosis (HP:0011651)
Term ID:
11651
Name:
Double outlet right ventricle with doubly committed ventricular septal defect and pulmonary stenosis
Synonym:
DORV with doubly committed VSD and pulmonary stenosis
Definition:
A double outlet right ventricle with a subaortic ventritricular septal defect (a hole between the two bottom chambers (ventricles) of the heart), that extends anterosuperiorly and are closely related to the pulmonary artery as well, are considered to be doubly committed. There is associated pulmonary stenosis, the abnormal narrowing or constriction of the pulmonary artery, in the main pulmonary artery and/or in the left or right pulmonary artery branches.